Succinylacetone-13C7

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Catalogue number:	PA STI 080300
Chemical name:	Succinylacetone-13C7
CAS Number:	NA
Alternate CAS Number:	51568-18-4 (Unlabelled)
Category:	miscellaneous compounds,stable isotopes
Synonyms:	4,6-Dioxoheptanoic Acid-13C7; NSC 174804-13C7; 4,6-Dioxoheptanoic-3,4,5,6,7-13C7 Acid;
Molecular form:	₁₃C₇H₁₀O₄
Appearance:	NA
Mol. Weight:	165.10
Storage:	2-8°C Refrigerator, Under inert atmosphere
Shipping Conditions:	Ambient
Applications:	Succinylacetone_x0000_-13C7 is a labelled analogue of Succinylacetone. Succinylacetone (SA) is a specific marker for the inherited metabolic disease, hepatorenal tyrosinemia. It was developed a stable-isotope for the determination of SA in dried blood spots (DBS) and liquid urine using a 13C4-SA as internal standard.The method was applied retrospectively and prospectively for the diagnosis of hepatorenal tyrosinemia and for follow-up of patients under treatment.