β-Hydroxyisovaleric acid

Stock Status : <%stockStatus%>

<%deliveryStatus%>

Catalogue number:	PA PHY 004274
Chemical name:	β-Hydroxyisovaleric acid
CAS Number:	625-08-1
Similar Products:	135236-72-5(calcium salt)
Category:	NA
Synonyms:	3-Hydroxy-3-methylbutyric; acid 3-Hydroxyisovaleric acid; 3-Methyl-3-hydroxybutyric acid; β-Hydroxy-β-methylbutyric acid; β-Hydroxyisovaleric acid; beta-Hydroxy beta-methylbutyric acid;
Molecular form:	C₅H₁₀O₃
Appearance:	Thick Clear Colourless Oil
Mol. Weight:	118.13
Storage:	2-8°C Refrigerator
Shipping Conditions:	Ambient
Applications:	?-Hydroxyisovaleric Acid is a metabolite of the essential amino acid Leucine and is synthesized in the human body. Studies suggest that ?-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated ?-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.